English Translation, Synonyms, Definitions and Usage Examples of Spanish Word ‘displasia fibrosa ósea’. Developmental, nonneoplastic disorder of bone-forming mesenchyme, causing bone maturation arrest at the woven bone stage; Usually. Join or Log Into Facebook. Email or Phone. Password. Forgot account? Log In. Do you want to join Facebook? Sign Up · Sign Up.
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Fibrous dysplasia FD is a non-neoplastic tumor-like congenital process, manifested as a localised defect in osteoblastic differentiation and maturation, with the replacement of normal bone with large fibrous stroma and islands of immature woven bone.
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Fibrous dysplasia has a varied radiographic appearance. If asymptomatic, it does not require treatment. The remainder of this article concerns itself with skeletal fibrous dysplasia. For a discussion of craniofacial fibrous dysplasia and cherubismplease refer to the respective articles.
In polyostotic form, patients usually present by 10 years old. There is no recognised gender predilection 9.
Displasia Ósea Florida: Reporte de Dos Casos y Revisión de la Literatura
The condition is often an incidental finding and is usually painless. Alternatively, it may present due to bony expansion or remodelling. Morbidity may arise from compression and displacement of adjacent structures. This is particularly true in craniofacial fibrous dysplasia, where the content of the orbit or cranial nerves may be compressed. Fibrous dysplasia is due to developmental dysplasia and focal arrest in normal firbosa activity secondary to a non-hereditary mutation which results in the diaplasia of all of the components of normal bone with a lack of normal differentiation into their mature structures.
Macroscopically, lesions are intramedullary and well circumscribed with abnormal whitish-grey color. Microscopically it manifests as large fibrous matrix with scattered curvilinear irregularly shaped trabeculae of immature, inadequately mineralized bone 6.
There is no vibrosa by osteoblasts differentiating feature from cemento-ossifying fibroma. It is usually asymptomatic until 2 nd -3 rd decade but can be seen throughout adulthood 6.
After puberty, the disease becomes inactive, and monostotic form does not progress to polyostotic form. As expected this presents earlier, typically in childhood mean age of 8 years with two-thirds symptomatic by the age of Ribs are the most common site of monostotic fibrous dysplasia.
Fibrous dysplasia of bone
Fibrous dysplasia is the most common cause of a benign expansile lesion of a rib see rib lesions. MRI is not particularly useful in differentiating fibrous dysplasia from other entities as there is marked variability in the appearance of the bone lesions, and they djsplasia often resemble a tumor or more aggressive lesions.
Demonstrates increased tracer uptake on Tc 99 bone scans lesions remain metabolically active into adulthood.
Usually, no treatment is required as the bone lesions usually do not progress beyond puberty. If a mass effect is severe, fibbrosa surgical decompression may be considered. The monostotic form does not transform or progress into the polyostotic form Not surprisingly, bone affected by fibrous dysplasia is weaker than normal and thus susceptible to pathological fractures.
It should be noted that many reported cases may relate to previous ribrosa with radiation therapy 6. Due to the variability of the appearance of fibrous dysplasia the potential differential is very long but will be significantly influenced by the dominant pattern.
Fibrous dysplasia of bone – Wikipedia
To quiz yourself on this article, log in to see multiple choice questions. The differential diagnosis for bone tumours is dependent on the age of the patient, with a very different set of differentials for the pediatric patient. You can psea scroll through stacks with your mouse wheel or the keyboard arrow keys.
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